2018 Board Review Pre-Test:
Cardiomyopathies IV: ARVC and Inherited

Cardiomyopathies IV: ARVC and Inherited - Anju Nohria, MD, MSc

Please complete this brief Pre-Test to give a baseline for learning .

Question Title

* 1. An 18 yo female dies suddenly during a karate class. She has no significant past medical history and no family history of cardiomyopathy or sudden cardiac death. She has 2 teenage brothers who are in good health. An autopsy shows ARVC.
Which of the following would you recommend to her brothers?

A. Primary prevention ICD without further testing

B. Genetic testing for ARVD regardless of clinical evaluation/findings

C. No participation in competitive sports

D. Screening history/exam, EKG/Holter, and echo/MRI every year regardless of test findings

Question Title

* 2. A 40 yo man presents with palpitations and syncope. EKG shows 1⁰ AVB and frequent PVCs. Echocardiogram shows mildly depressed EF (45-50%). His family history is notable for mother having sick sinus syndrome and PPM at age 76, maternal grandfather died of PE at age 50, and maternal uncle had HF and SCD at age 54.
Which of the following is the next most appropriate step in his evaluation?

A. Evaluate for lyme, sarcoid, and giant cell myocarditis

B. Send genetic testing for LMNA cardiomyopathy

C. Place an ICD given his strong family history

D. A and B

Question Title

* 3. A 40 yo woman presents w/ new onset DOE. Echo shows EF 30% and LV non-compaction (NC/C ratio 4). In addition to GDMT, which of the following would you recommend?

A. 3 generation family history and genetic testing

B. 24 ambulatory Holter monitor

C. Anti-coagulation for prevention of thromboembolism

D. All of the above

Question Title

* 4. Please provide your first and last name.
Pre-test questions will not be scored, your name is required solely to confirm completion.

First Name *

Last Name